Nefrectomia Radical com Trombectomia da Veia Cava Laparoscópica num Caso de Feocromocitoma Maligno

Autores

DOI:

https://doi.org/10.24915/aup.37.1-2.162

Palavras-chave:

Feocromocitoma, Laparoscopia, Nefrectomia, Procedimentos Cirúrgicos Robóticos, Trombectomia, Veia Cava Inferior

Resumo

Os feocromocitomas com trombo na veia cava são entidades extremamente raras, estando poucos casos descritos na literatura. Apesar da nefrectomia radical com adrenalectomia/suprarrenalectomia e trombectomia da veia cava inferior (VCI) corresponder ao tratamento de escolha, esta é uma técnica cirúrgica desafiante com uma abordagem ainda não padronizada. Apresenta-se um caso de um homem de 49 anos com diagnóstico incidental de um feocromocitoma localmente invasivo, com trombo na VCI nível 1. Foi proposta uma nefrectomia radical direita laparoscópica com adrenalectomia/suprarrenalectomia, trombectomia da VCI e cavorrafia. Neste artigo faz-se uma descrição detalhada da técnica cirúrgica e uma comparação com as estratégias atualmente utilizadas no tratamento do feocromocitoma. Tumores renais e suprarrenais/adrenais com trombo na veia cava estão associados a maior morbilidade e mortalidade, sobretudo no caso do feocromocitoma. Apesar de complexa, a cirurgia minimamente invasiva é uma opção segura no contexto de uma equipa experiente e multidisciplinar.

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Biografia Autor

Tito Palmela Palmela Leitão, Univerdade de Lisboa - Faculdade de Medicina

Urology

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Publicado

2022-01-26

Edição

Secção

Case Report